We hereby describe a case of 38 years old young man, known diabetic and alcoholic, presenting with history of pain in right hypochondriam, fever and progressive jaundice. His investigations revealed marked derangement of liver functions with predominant conjugated hyperbilirubinemia and raised alkaline phosphatase suggestive of obstructive jaundice. Subsequent investigation by ultrasound and magnetic resonance cholangiopancreatography (MRCP), revealed a large stone in the cystic duct compressing the common bile duct with intrahepatic biliary radical dilatation, suggesting the rare diagnosis of Mirizzi Syndrome. In the present report the authors will discuss the importance of recognizing this relatively rare entity, its classification and management related issues.

Keywords: Obstructive Jaundice, Hyperbilirubinemia, Mirizzi syndrome, Gallstone