Indian Journal of Clinical Anaesthesia


Anaesthetic management in Pierre Robin syndrome with bicuspid aortic valve: A case report


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Article Type : Case Report

Author Details: Shobha V*,Saurabh Mittal,K V. Rawat

Volume : 6

Issue : 3

Online ISSN : 2394-4994

Print ISSN : 2394-4781

Article First Page : 473

Article End Page : 475


Abstract

Pierre Robin Sequence (PRS) is an uncommon complex congenital syndrome with a clinical triad of micrognathia, glossoptosis and cleft palate posing a risk of upper airway obstruction and difficulty in feeding with or without multiple secondary abnormalities. We report a case of 3.5yr male child suffering from PRS along with left renal agenesis, bilateral CTEV, bilateral inguinal hernia, pectus carinatum, bicuspid aortic valve where successful ventilation and intubation was done and taking a tongue stitch along with nebulization and prone position helped to maintain airway during recovery.

Keywords: Pierre robin syndrome, Bicuspid aortic valve, Cleft palate.

Doi :-https://doi.org/10.18231/j.ijca.2019.091