International Journal of Oral Health Dentistry


Noonan syndrome: A case report


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Author Details: Haifaa Al Qabbani

Volume : 3

Issue : 4

Online ISSN : 2395-499X

Print ISSN : 2395-4914

Article First Page : 238

Article End Page : 239


Abstract

Noonan syndrome is a developmental disorder which is characterized by ocular, facial, cardiac, and dental anomalies. The etiology of Noonan syndrome is unknown. This may result due to either complete or partial absence of an X-chromosome or could be genetic effect. Dental features of the Noonan syndrome that have been described includes: malocclusion, greater risk of caries, in a greater proportion of subjects, while odontogenic keratocyst or giant cells lesions in a smaller proportion. The aim of the current article is to present the oro‑facial findings in a case with Noonan syndrome in a 7 year‑old male. Multidisciplinary treatment is the key to success in managing children with Noonan syndrome. Pediatric dentists play a significant role in leading the health team.

Keywords: Noonan syndrome, Dental, High arch palate.