IP International Journal of Ocular Oncology and Oculoplasty

Spontaneous intraorbital arteriovenous fistula with thrombosed varix: A rare case report

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Author Details: Sucheta Parija, Indranil Saha

Volume : 3

Issue : 1

Online ISSN : 2581-5016

Print ISSN : 2581-5024

Article First Page : 98

Article End Page : 100


Arteriovenous shunts in the orbit are rare acquired vascular malformations and cause of proptosis. Literature search reported only 6 spontaneous and 4 traumatic cases of intraorbital AVF. We report the clinical and radiological findings of a patient with isolated, spontaneous AVF of orbit with a thrombosed varix which is rare and its management dilemma. A 55 year old female presented with progressive axial proptosis, chemosis and loss of vision in the right eye. There was no preceding history of trauma or any systemic illness. Imaging of the brain and orbit was suggestive of an intraorbital arteriovenous fistula which had perhaps evolved spontaneously into a thrombosed varix of the right superior ophthalmic vein due to pooling of blood which explained the mass effect features. The thrombosed SOV was excised by frontal craniotomy, following which the symptoms subsided with partial restoration of vision.

CT angiography, Orbital AVF, Proptosis, Thrombosed varix