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IP Journal of Diagnostic Pathology and Oncology


Darier’s Disease: A rare genodermatosis


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Article Type : Case Report

Author Details: Divya V*,Sudha V

Volume : 4

Issue : 2

Online ISSN : 2581-3706

Print ISSN : 2581-3714

Article First Page : 153

Article End Page : 155


Abstract

Darier’s disease or darier white disease or keratosis follicularis is a rare inherited autosomal dominant genodermatosis which are clinically characterized by multiple hyperpigmented, firm , greasy, warty lesion usually in seborrhoeic distribution. They also show palmar pits, and mucosal involvement. Histologically they present with suprabasal splitting of epidermis with presence of acnatholytic and dyskeratotic cells. we report a case of a female of 30years old who shows clinical and histological features of dariers disease.

Keywords: Genodermatosis , Darier’s disease, Keratotic papules, Dyskeratosis, Hyperpigmented papules.

Doi :-https://doi.org/10.18231/j.jdpo.2019.032