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Indian Journal of Clinical Anaesthesia


Prader willi syndrome- A case report


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Author Details : Shilpa H. L., Shwetha Odeyar S., Adarsh E. S.

Volume : 5, Issue : 2, Year : 2018

Article Page : 297-298


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Abstract

Prader willi syndrome (PWS) is a complex multisystem disorder. PWS mainly affects central nervous system and often involves the hypothalamus. Its major clinical features include neonatal hypotonia, developmental delay, short stature, behavior abnormalities, childhood onset obesity, hypothalamic hypogonadism and characteristic appearance.
Anaesthetic management with general or regional anaesthesia for these patients is difficult mainly due to morbid obesity. The importance of PWS for anesthesiologist and primary physician is estimated by the circumstances as the prevalence of PWS is nearly as frequent as trisomy -21. We report the anaesthetic management of a 22 year old male patient with genetically proven PWS (small stature, obesity with characteristic behaviour problem) who presented with chronic fissure in ano. Though the clinical course of the patient was uneventful under saddle block. In this case report we discuss our strategy for the prevention of perioperative complications for PWS patients.

Keywords: Prader willi syndrome.

Doi : 10.18231/2394-4994.2018.0057

How to cite : Shilpa H. L., Shwetha Odeyar S., Adarsh E. S., Prader willi syndrome- A case report. Indian J Clin Anaesth 2018;5(2):297-298

Copyright © 2018 by author(s) and Indian J Clin Anaesth. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (CC BY 4.0) (creativecommons.org)